Granulomatosis with polyangiitis and Kartagener’s syndrome

Authors

DOI:

https://doi.org/10.15381/anales.v85i2.27009

Keywords:

Granulomatosis with Polyangiitis, Kartagener Syndrome

Abstract

We present a 42-year-old woman with a 1-year history of chronic rhinosinusitis, left facial palsy, bilateral sensorineural hearing loss, and bilateral necrotizing scleritis. Analytics revealed, elevated C-reactive protein and positive anti-proteinase 3. Tomography showed varicose and cystic bronchiectasis in both lungs and situs inversus totalis. It was concluded that the clinical assessment was compatible with Granulomatosis with polyangiitis in a patient with Kartagener’s Syndrome. She received immunosuppressive treatment with rituximab and high-dose corticosteroids. The evolution was partially favorable, because the patient already had irreversible organ damage at the time of diagnosis.

Author Biographies

  • Mayra Paredes, Hospital Nacional Dos de Mayo, Servicio de Reumatología. Lima, Peru

    Médico especialista en reumatología.

  • Jimena Hidalgo, Hospital Nacional Dos de Mayo, Servicio de Reumatología. Lima, Peru

    Médico especialista en reumatología.

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Published

2024-05-13

Issue

Section

Reporte de Casos

How to Cite

1.
Paredes M, Hidalgo J. Granulomatosis with polyangiitis and Kartagener’s syndrome. An Fac med [Internet]. 2024 May 13 [cited 2024 Jun. 26];85(2). Available from: https://revistasinvestigacion.unmsm.edu.pe/index.php/anales/article/view/27009