An unusual presentation of hypoglycemic distal polyneuropathy caused by an insulinoma in the context of multiple endocrine neoplasia 1
DOI:
https://doi.org/10.15381/anales.v79i4.15637Keywords:
Multiple Endocrine Neoplasia Type 1, Hypoglycemia, Polyneuropathies, Insulinoma, ChordomaAbstract
Multiple endocrine neoplasia type 1 is a rare disease. It is characterized by the neuroendocrine, parathyroid, pituitary, and enteropancreatic tumor involvement. We present the case of a 19 year old patient with symptoms of headache, convulsions and weakness of the four extremities. The presence of hypoglycemia 33mg/dL was confirmed. The electromyographic study showed motor sensory polyneuropathy in all four extremities. The abdominal magnetic resonance showed a tumor in the tail of the pancreas that after the pancreatectomy was confirmed as insulinoma. The glycemia was normalized. In addition, he presented a pituitary macroadenoma, primary hyperparathyroidism and non-functioning adrenal tumor. At 25 years of age, he presented severe headache and amaurosis of the right eye. Axial tomography showed a giant pituitary tumor and in the study of pathology chondroid malignancy (chordoma) was diagnosed.Downloads
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2018-12-30
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Reporte de Casos
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1.
Castillo Sayán O, Medina Sánchez C, Verona Rubio R, Machicado Zuñiga E, Mendoza Pérez G, Tello Cebreros L. An unusual presentation of hypoglycemic distal polyneuropathy caused by an insulinoma in the context of multiple endocrine neoplasia 1. An Fac med [Internet]. 2018 Dec. 30 [cited 2024 Jul. 17];79(4):317-22. Available from: https://revistasinvestigacion.unmsm.edu.pe/index.php/anales/article/view/15637